World Journal of Surgical Research Volume No 6

Original Article Open Access

A Rare Case of Servelle Martorelle Syndrome- Extensive Angio-osteohypotrophic Lesion of Upper Limb

Ankur Bhatnagar, Mayuresh Deshpande and V D Upadhya
World Journal of Surgical Research 2012, 1:2

Abstract

Background: Servelle Martorelle Syndrome (SMS) is a congenital vascular malformation associated with soft tissue hypertrophy and bony hypoplasia. This rarely involves whole of an extremity, with involvement of part of limbs reported in literature.

Case Report: We present a case of a twelve year boy with history of circumferential soft tissue hypertrophy involving whole of left upper limb, scapular region and axilla since birth. The entire left upper limb length was lesser than the right upper limb.

Conclusions: This is a very rare case of Servelle Martorelle Syndrome having extensive limb involvement at a very young age. Highlighted is the role of conservative treatment and close follow-up to understand the natural history of the diseases, with prompt treatment of complications.




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