World Journal of Pathology Volume No 6

Case Report Open Access

Pyelonephritis Complicating a Multicystic Dysplastic Kidney with Ipsilateral Megaureter: Initial Presentation in an Adult

Sanjay Marwah, Nisha Marwah, Hem Kant Verma, Jyotsna Sen, Shilpa Garg, Rachneet Kohli and Hardeep Singh
World Journal of Pathology 2014, 3:11



Multicystic dysplastic kidney (MCDK) is a rare congenital anomaly that usually presents as neonatal abdominal mass. It presents as a unilateral disorder and ipsilateral ureter is atretic. Its presentation in adults is even rarer due to its involution during initial years of life. In present case, an adult patient presented with renal MCDK with ipsilateral obstructed megaureter that led to pyelonephritis.

Case Report

A 55-year-old male presented with loin pain of one month duration. Imaging studies revealed non functioning right kidney with ipsilateral megaureter. The patient underwent right nephroureterectomy and on histopathology, the diagnosis of MCDK with pyelonephritis was made.


MCDK associated with ipsilateral obstructed megaureter is an extremely unusual presentation in adult patients. Association of pyelonephritis with MCDK is even rarer.


Multicystic dysplastic kidney, pyelonephritis, megaureter, adult.

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